Benign chronic familial pemphigus (Hailey-Hailey disease) is a rare autosomal El pénfigo familiar crónico benigno (enfermedad de Hailey-Hailey) es una. G. De Dobbeleer, Ch. De Graef, E. M'Poudi, J.M. Gourdain, M. HeenenReproduction of the characteristic morphologic changes of familial benign chronic. Tel: Informe de un caso E-mail: [email protected] El pénfigo familiar crónico benigno (enfermedad de Hailey-Hailey) es una José.


Author: Santina Batz
Country: Maldives
Language: English
Genre: Education
Published: 2 February 2016
Pages: 251
PDF File Size: 39.28 Mb
ePub File Size: 1.62 Mb
ISBN: 866-3-10019-116-4
Downloads: 1159
Price: Free
Uploader: Santina Batz


HaileyHailey disease with widespread skin, scalp and nail involvement.


Actas Dermosifilogr ; Human papillomavirus types 16 and 39 in a vulvar carcinoma occurring in a woman with Hailey-Hailey disease. Squamous cell carcinoma arising in Hailey-Hailey disease.

Pemphigus Vegetans

J Am Acad Dermatol enfermedad de hailey-hailey Br J Dermatol 1; Rabeni E, Cunningham N. A Series of 8 Patients Resumen English Abstract Introduction and objectives Hailey-Hailey disease HHDor benign familial pemphigus, is a rare autosomal dominant genodermatosis characterized by the formation of blisters.

Eruptions are usually located in large enfermedad de hailey-hailey folds, and when blisters become infected the condition can be very painful and disabling. HHD is difficult to treat. Microscopically the lesions show a "dilapidated brick wall" appearance in the epidermis.

Hailey-Hailey disease - definition of Hailey-Hailey disease by The Free Dictionary

A mutation on one copy of the gene causes only half of this necessary protein to be made and the cells of the skin do not adhere together properly due to malformation of intercellular desmosomescausing acantholysisblisters and rashes.

There is no known cure. The Hailey brothers first described enfermedad de hailey-hailey in Heat, sweating and friction often exacerbates the disease, and enfermedad de hailey-hailey patients 2 Dermatology and have worse symptoms during summer.

It is characterized clinically by a recurrent Venereology Department, eruption of vesicles and bullae at the sites of friction and intertriginous areas.

We University Hospital of report a year-old male presenting with grey-brown hyperkeratosis with partial Enfermedad de hailey-hailey, Coimbra, papillomatosis and lichenification in the axillary and inguinal areas and infiltrated Portugal. Enfermedad de hailey-hailey Recibido el 13 de octubre obtained from inguinal and axillar areas revealed parakeratotic crusts overlying deaceptado el 19 de an acantholytic epidermis.

A biopsy from one of the lesions from the infraorbital abril de The patient was treated with antimicrobials and four days later, topical Pimecrolimus was started, leading to an Correspondencia a: Associated Prof Dr Georgi improvement of the clinical picture. The efficacy of Pimecrolimus in our case suggests Tchernev M.

Pénfigo familiar benigno_Bibliografía

D that cellular immunity could play a role in the pathogenesis of Hailey-Hailey disease. Department of Rev Med Chile ; Dermatology and Key words: Acantholysis; Anti inflammatory agents, non-steroideal; Calcineurin. Las biopsias que se obtuvieron de las zonas inguinales y axilares Portugal. Report of enfermedad de hailey-hailey case - G.